Isolated Left Ventricular Apical Hypoplasia with Infundibular Pulmonary and Aortic Stenosis: a Rare Combination
نویسندگان
چکیده
Isolated left ventricular (LV) apical hypoplasia is a rare congenital cardiac anomaly which is not accompanied by other cardiac abnormalities, with the exception of two cases. We report a case of a 33-year-old male patient with isolated LV apical hypoplasia combined with infundibular pulmonary stenosis and aortic stenosis. We review a literature focusing on the characteristic magnetic resonance features and combined cardiac abnormalities.
منابع مشابه
Congenital Aortic Stenosis
Of 3,022 patients with congenital heart disease studied in the heart clinic of the Royal Liverpool Children's Hospital during the last five years, 120 presented with signs of uncomplicated aortic stenosis giving an incidence of 4% of all cases of congenital heart disease. Swan, Wilkinson, and Blount (1958) noted an incidence of 5% of all patients in their congenital heart disease clinic. It has...
متن کاملTricuspid aortic stenosis with systolic dysfunction in a 14-year-old boy: Critical stenosis, noncompaction or secondary fibroelastosis?
A bicuspid aortic valve is the most common cause of isolated valvular aortic stenosis in the pediatric age group; another cause is annular hypoplasia, with the tricuspid valve being the least commonly involved. In aortic stenosis, causes of systolic dysfunction are critical stenosis, secondary fibroelastosis and noncompaction. Critical stenosis is diagnosed in the usual fashion. Secondary fibro...
متن کاملProphylactic Irradiation of the Lung
Situs inversus totalis is a rare congenital anomaly, as demonstrated by mass radiographic screening in Norway which yielded an incidence of 1 in 10,000.@ Single coronary artery is also rare; a recent review suggested an incidence of 4 in 10,000.' The chance of these two lesions occurring simultaneously is thus about 4 in 1 x 108. Hypertrophic subaortic stenosis is uncommonly as sociated with ot...
متن کامل[Lecompte procedure in a case of anatomically corrected L-malposition of the great arteries].
We present the case of a 12-month-old patient, echocardiographically diagnosed with tetralogy of Fallot, with indications for surgical treatment due to cyanosis. In the hemodynamic study, subaortic interventricular communication (IVC) was found as well as aortic override, infundibular, valvular, and supravalvular pulmonary stenosis, together with L-malposition of the great arteries and the righ...
متن کاملCriss-cross heart with dextrocardia and transposition of the great arteries: a rare pathology.
A 16-year-old male patient who underwent bilateral modified Blalock-Taussig shunt operation at the age of 6 was admitted to our clinic with cyanosis. The oxygen saturation was 60% at time of admission. Echocardiography and computed tomography revealed situs solitus dextrocardia with concordant atrioventricular (AV) discordant ventriculoarterial relation and obstructed bilateral Blalock-Taussig ...
متن کامل